Moyamoya Syndrome as a Severe Cerebrovascular Complication of Mucopolysaccharidosis Type I: Clinical Presentation and Underlying Mechanisms

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Figure 1: Computed tomography angiography of the supra-aortic and cerebral vessels showing long occlusions of both internal carotid arteries (black arrow) with extensive collateral vascular networks consistent with Moyamoya syndrome (red asterisk) in a patient with mucopolysaccharidosis type I
Published Jul 12, 2026
https://doi.org/10.62438/tunismed.v104i07.6678
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Vol. 104 No. 07 (2026): Tunis Med Jul 2026

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Karima Daghor-Abbaci
Internal medicine department, Bab El Oued University Hospital center, Bab El Oued city, Faculty of Medicine, University of health sciences, Algiers, Algeria
https://orcid.org/0000-0002-5669-5759
Radhia Ait Chalal
Radiology department, Bab El Oued University Hospital center, Bab El Oued city, Faculty of Medicine, University of health sciences, Algiers, Algeria
Hind Arzour
Nephrology Department, Mustapha Bacha University Hospital Center, University of health sciences, Algiers, Algeria
Assia Haddouche
Rheumatology department, Benaknoun University Hospital center, Faculté of Medicine, University of health sciences, Algiers, Algeria
Houria Saoula
Department of Hepato-gastro-enterology, Bab El Oued University Hospital center, Bab El Oued city, Algiers, Algeria
Nazim Laraba
Internal medicine department, Bab El Oued University Hospital center, Bab El Oued city, Faculty of Medicine, University of health sciences, Algiers, Algeria

Abstract

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